Essential first-line test for suspected acute porphyria in adults. Use in determining metabolic response to IV hematin.
Quantitative Ion Exchange Chromatography/Spectrophotometry
Protect from light. Transfer an 8 mL aliquot from a well-mixed collection to ARUP Amber Transport Tubes. (Min: 3.5 mL)
Body fluids other than urine.
Ambient: Unacceptable; Refrigerated: 4 days; Frozen: 1 month
|Porphobilinogen (PBG), Urine-per volume||0.0-8.8 µmol/L|
|Porphobilinogen, Rndm Urn-ratio to CRT||No reference interval (mg/g crt)|
Compliance Statement B: For laboratory developed tests not using a RUO kit, and for FDA approved, cleared or 510(k) exempt assays with alterations. This test was developed and its performance characteristics determined by ARUP Laboratories. The U. S. Food and Drug Administration has not approved or cleared this test; however, FDA clearance or approval is not currently required for clinical use. The results are not intended to be used as the sole means for clinical diagnosis or patient management decisions.
Appropriate test to rule out acute intermittent porphyria (AIP) and other acute attacks of other types of porphyrias associated with neurologic and/or psychiatric symptoms.
|Component Test Code*||Component Chart Name||LOINC|
|0020207||Creatinine, Urine - per volume||2161-8|
|0080262||Porphobilinogen (PBG), Urine -per volume||2811-8|
|2011477||Porphobilinogen, Rndm Urn-ratio to CRT||13797-6|
- PBG, Quantitative
- Watson-Schwartz Test