Ordering Recommendation

Use to MONITOR glycosaminoglycans (GAGs) in patients previously diagnosed with a mucopolysaccharidosis (MPS). Approval by an ARUP genetic counselor or medical director required BEFORE ordering this test. To screen for MPS, refer to Mucopolysaccharides Screen - Electrophoresis & Quantitation, Urine (0081352).

New York DOH Approval Status

This test is New York state approved.

Specimen Required

Patient Preparation

Morning void is preferred.

Collect

Urine.

Specimen Preparation

Transfer 10 mL urine to ARUP Standard Transport Tubes and freeze immediately. (Min: 5 mL)

Storage/Transport Temperature

Frozen.

Unacceptable Conditions

Contaminated specimens. Specimens containing preservatives.

Remarks
Stability

Ambient: Unacceptable; Refrigerated: Unacceptable; Frozen: 1 month (avoid repeated freeze/thaw cycles)

Methodology

Spectrophotometry

Performed

Tue

Reported

3-9 days

Reference Interval

0-5 months: 14.6-47.8 mg/mmol creatinine
6-11 months: 3.7-35.5 mg/mmol creatinine
1-2 years: 5.4-30.8 mg/mmol creatinine
3-6 years: 5.2-16.7 mg/mmol creatinine
7-13 years: 2.4-10.2 mg/mmol creatinine
14 years or older: 0.0-7.1 mg/mmol creatinine

Interpretive Data

This test was developed and its performance characteristics determined by ARUP Laboratories. It has not been cleared or approved by the US Food and Drug Administration. This test was performed in a CLIA certified laboratory and is intended for clinical purposes.

Compliance Category

Laboratory Developed Test (LDT)

Note

Hotline History

N/A

CPT Codes

83864

Components

Component Test Code* Component Chart Name LOINC
0081355 Mucopolysaccharides mg/mmol CRT 46132-7
* Component test codes cannot be used to order tests. The information provided here is not sufficient for interface builds; for a complete test mix, please click the sidebar link to access the Interface Map.

Aliases

  • Chondroitin Sulfate
  • Dermatan Sulfate
  • GAG(s)
  • Glycosaminoglycans
  • Heparan Sulfate
  • Urine glycosaminoglycans
Mucopolysaccharides, Quantitative, Urine