Acylcarnitine Quantitative Profile, Plasma
Ordering Recommendation

Diagnose and monitor for fatty acid oxidation disorders and organic acidemias. Use in conjunction with urine organic acids and acylglycines testing.

Tandem Mass Spectrometry
Tue, Thu, Sat
2-7 days
New York DOH Approval Status
This test is New York DOH approved.
ARUP Consult®
Disease Topics
Specimen Required
Patient Preparation
Green (sodium or lithium heparin). Also acceptable: Plain red. 
Specimen Preparation
Separate serum or plasma from cells ASAP or within 2 hours of collection. Transfer 0.5 mL serum or plasma to an ARUP Standard Transport Tube and freeze immediately. (Min: 0.2 mL) Avoid hemolysis. 
Storage/Transport Temperature
CRITICAL FROZEN. Separate specimens must be submitted when multiple tests are ordered. 
Unacceptable Conditions
Room temperature specimens. Specimens that have been refrigerated for longer than 12 hours. Grossly hemolyzed specimens. 
Clinical information is needed for appropriate interpretation. Additional required information includes age, gender, diet (eg, TPN therapy), drug therapy, and family history. Biochemical Genetics Patient History Form is available on the ARUP Web site at or by contacting ARUP Client Services. 
After separation from cells: Ambient: Unacceptable; Refrigerated: 12 hours; Frozen: 1 month (avoid repeated freeze/thaw cycles) 
Reference Interval
Reports include age appropriate reference intervals and interpretation.
Interpretive Data

Compliance Statement B: For laboratory developed tests not using a RUO kit, and for FDA approved, cleared or 510(k) exempt assays with alterations. This test was developed and its performance characteristics determined by ARUP Laboratories. The U. S. Food and Drug Administration has not approved or cleared this test; however, FDA clearance or approval is not currently required for clinical use. The results are not intended to be used as the sole means for clinical diagnosis or patient management decisions.

Hotline History
Component Test Code*Component Chart NameLOINC
0040029C5-OH, 3-OH Isovaleryl39001-3
0040034Acylcarnitine, Plasma Interpretation46252-3
0040037C2, Acetyl30191-1
0040038C3, Propionyl30551-6
0040039C4, Iso-/Butyryl51413-3
0040042C5, Isovaleryl/2Mebutyryl30531-8
0040046C5-DC, Glutaryl30349-5
0040047C6, Hexanoyl30358-6
0040049C8, Octanoyl30540-9
0040054C8:1, Octenoyl30541-7
0040057C10, Decanoyl30327-1
0040058C10:1, Decenoyl30328-9
0040062C12, Dodecanoyl30331-3
0040063C12:1, Dodecenoyl30332-1
0040064C12-OH, 3-OH-Dodecanoyl30233-1
0040066C14, Tetradecanoyl30565-6
0040067C14:1, Tetradecenoyl30566-4
0040068C14:2, Tetradecadienoyl30564-9
0040069C14-OH, 3-OH-Tetradecanoyl30238-0
0040074C14:1-OH, 3-OH-Tetradecenoyl30190-3
0040076C16, Palmitoyl30356-0
0040077C16:1, Palmitoleyl30357-8
0040078C16-OH, 3-OH-Palmitoyl30234-9
0040079C16:1-OH, 3-OH-Palmitoleyl30235-6
0040087C18, Stearoyl30560-7
0040093C18:1, Oleyl30542-5
0040094C18:2, Linoleyl30534-2
0040097C18-OH, 3-OH-Stearoyl35656-8
0040098C18:1-OH, 3-OH-Oleyl30312-3
0040101C18:2-OH, 3-OH-Linoleyl30237-2
* Component test codes cannot be used to order tests. The information provided here is not sufficient for interface builds; for a complete test mix, please click the sidebar link to access the Interface Map.
  • ACP profile
  • acylcarnities, quantitative
  • acylcarnitine profile
  • plasma acylcarnitine profile