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Succinylacetone, Quantitative, Urine
Ordering Recommendation
For accurate quantitation of succinylacetone at diagnosis, organic acids recommended as initial or concurrent test. Monitor individuals with tyrosinemia type 1 who are on therapy. To rule out or diagnose tyrosinemia type 1, refer to Organic Acids, Urine (0098389) and Amino Acids Quantitative by LC-MS/MS, Plasma (2009389).
New York DOH Approval Status
Specimen Required
Random urine. (First morning urine is preferred.)
Transfer 1.0 mL urine to an ARUP standard transport tube and freeze immediately. (Min: 0.3 mL)
CRITICAL FROZEN. Separate specimens must be submitted when multiple tests are ordered.
Ambient specimens. Specimens exposed to more than one freeze/thaw cycle.
Clinical information is needed for appropriate interpretation. Submit age, gender, diet (e.g., TPN therapy), drug therapy, and family history on a Biochemical Genetics Patient History Form available at www.aruplab.com/patienthistory or by contacting ARUP Client Services at 800-522-2787.
Ambient: Unacceptable; Refrigerated: 24 hours; Frozen: 1 month
Methodology
Liquid Chromatography-Tandem Mass Spectrometry
Performed
Wed
Reported
4-12 days
Reference Interval
0.000-0.300 mmol/mol CRT
Interpretive Data
Laboratory Developed Test (LDT)
Note
Hotline History
CPT Codes
83921
Components
| Component Test Code* | Component Chart Name | LOINC |
|---|---|---|
| 2007402 | Succinylacetone Quant Urine | 25137-1 |
| 2007404 | Creatinine (Succinylacetone), Urine | 2161-8 |
| 2007405 | Succinylacetone Quant Urine, Interpret. | 48767-8 |
Aliases
- succinylacetone levels
- succinylacteone concentration
